Anesthesiology and Pain Medicine

Published by: Kowsar

Anesthetic Management in a Child With Citrullinemia: A Case Report

Mohammad Gharavifard 1 , Alireza Sabzevari 2 , * and Reza Eslami 1
Authors Information
1 Department of Anesthesiology, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran
2 Surgical Oncology Research Center, Mashhad University of Medical Sciences, Mashhad, Iran
Article information
  • Anesthesiology and Pain Medicine: August 01, 2014, 4 (3); e21791
  • Published Online: August 13, 2014
  • Article Type: Case Report
  • Received: July 7, 2014
  • Revised: July 16, 2014
  • Accepted: July 27, 2014
  • DOI: 10.5812/aapm.21791

To Cite: Gharavifard M, Sabzevari A, Eslami R. Anesthetic Management in a Child With Citrullinemia: A Case Report, Anesth Pain Med. 2014 ; 4(3):e21791. doi: 10.5812/aapm.21791.

Copyright © 2014, Iranian Society of Regional Anesthesia and Pain Medicine (ISRAPM). This is an open-access article distributed under the terms of the Creative Commons Attribution-NonCommercial 4.0 International License ( which permits copy and redistribute the material just in noncommercial usages, provided the original work is properly cited.
1. Introduction
2. Case Presentation
3. Discussion
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  • 2. Tomomasa T, Kobayashi K, Kaneko H, Shimura H, Fukusato T, Tabata M, et al. Possible clinical and histologic manifestations of adult-onset type II citrullinemia in early infancy. J Pediatr. 2001; 138(5): 741-3[DOI][PubMed]
  • 3. Ohura T, Kobayashi K, Tazawa Y, Abukawa D, Sakamoto O, Tsuchiya S, et al. Clinical pictures of 75 patients with neonatal intrahepatic cholestasis caused by citrin deficiency (NICCD). J Inherit Metab Dis. 2007; 30(2): 139-44[DOI][PubMed]
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  • 8. Davis PJ, Cladis FP, Motoyama EK. Smith's Anesthesia for Infants and Children: Expert Consult Premium. 2010;
  • 9. Ujihira N, Ohya M, Mabuchi C, Indo T, Hashizume Y. [An autopsied case of type II citrullinemia--transient effectiveness with either citrate or benzoate to the consciousness disturbance]. Rinsho Shinkeigaku. 1989; 29(4): 436-41[PubMed]
Creative Commons License Except where otherwise noted, this work is licensed under Creative Commons Attribution Non Commercial 4.0 International License .

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